An Unexpected Case of Isolated Left Ventricular Apical Hypoplasia in an Asymptomatic Patient

Authors

  • Rachel Anne Xuereb Mater Dei Hospital, Malta
  • Sara Xuereb Mater Dei Hospital
  • Tiziana Felice Mater Dei Hospital
  • Mariosa Xuereb Mater Dei Hospital
  • Alex Borg Mater Dei Hospital

DOI:

https://doi.org/10.17987/icfj.v20i0.675

Keywords:

Isolated left ventricular apical hypoplasia, Cardiac MRI, Congenital, Rare, Asymptomatic

Abstract

Isolated left ventricular (LV) apical hypoplasia is a rare type of congenital heart disease. It is often asymptomatic in childhood but may lead to complications later on in life. The proposed mechanism is inadequate LV dilatation during development of the primitive ventricle, resulting in a spherical LV. To our knowledge, we describe for the first time a case of isolated LV apical hypoplasia in an asymptomatic patient, diagnosed on investigation of an abnormal 12-lead resting electrocardiogram (ECG).

Author Biographies

Rachel Anne Xuereb, Mater Dei Hospital, Malta

Department of Medicine, Basic Specialist Trainee

Sara Xuereb, Mater Dei Hospital

Department of Cardiology, Higher Specialist Trainee

Tiziana Felice, Mater Dei Hospital

Department of Cardiology, Consultant Cardiologist

Mariosa Xuereb, Mater Dei Hospital

Department of Cardiology, Consultant Cardiologist

Alex Borg, Mater Dei Hospital

Department of Cardiology, Consultant Cardiologist

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Published

2020-08-07

Issue

Section

Letters to the Editor