Pulmonic Papillary Fibroelastoma: Cause of Recurrent Pulmonary Emboli and Treatment


  • Alexander Eugene Urban University of Tennessee Health Science Center
  • Masoor Kamalesh Indiana University School of Medicine
  • Daniel Gutteridge Indiana University School of Medicine




papillary fibroelastoma, pulmonary valve, pulmonary embolus, anticoagulation


Cardiac papillary fibroelastomas are rare, typically benign primary cardiac tumors.  The pulmonary valve is the least common site for valvular papillary fibroelastomas.  They commonly present with dyspnea on exertion and can show right ventricular outflow tract obstruction on echocardiography.  Embolic phenomena are one of the most serious consequences.  Treatment usually consists of surgical excision.  We report the first case of pulmonary emboli from pulmonary valve papillary fibroelastoma treated with anticoagulation.  This occurred in only the second case of pulmonary emboli from pulmonary papillary fibroelastoma reported in literature to date.

Author Biographies

Masoor Kamalesh, Indiana University School of Medicine

Cardiology, Chief

Daniel Gutteridge, Indiana University School of Medicine

Pulmonary Critical Care


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