Hoarseness of Voice as a Primary Presentation of Pulmonary Hypertension: a Rare case of Ortner’s (Cardio-vocal) Syndrome
Keywords:Ortner’s syndrome, Pulmonary hypertension, Vocal cord palsy.
Ortner’s (cardio-vocal) syndrome is a rare disease entity that involves compression of the left recurrent laryngeal nerve due to enlargement of cardiovascular structures. The syndrome was first described by Norbert Ortner (an Austrian physician) in 1897 and is usually reported to be associated with mitral stenosis. However, we report a rare case when a 20-year-old girl presented with hoarseness of voice and was found to have an enlarged main pulmonary trunk due to pulmonary hypertension that was compressing the left recurrent laryngeal nerve. The case highlights a rare presentation of a relatively common disease and stresses the importance of detailed cardiac workup in a patient with hoarseness of voice. We present the case and review the literature.
Ramadan HH, Wax MK, Avery S. Outcome and changing cause of unilateral vocal cord paralysis. Otolaryngol Head Neck Surg 1998; 118:199-202.
Ortner N. Recurrent nerve palsy in patient with mitral stenosis (in German). Wien Klin Wochenschr. 1897;10:753-5.
Fetterolf G, Norris G. The anatomical explanation of paralysis of left recurrent laryngeal nerve found in certain case of mitral stenosis. Am J Med Sci. 1911;141:625e638.
Shi-Min Yuan. Ortner (cardio-vocal) syndrome: a collective review. Kuwait Medical Journal 2014; 46(1):3-13.
Panwar CSS, Mehta LCAK, Verma SCRK. High-altitude induced Ortner’s syndrome. Med J Armed Forces India 2004; 60:182-183.
Stoob K, Alkadhi H, Lachat M. Resolution of hoarseness ater endovascular repair of thoracic aortic aneurysm: a case of Ortner’s syndrome. Ann Otol Rhinol Laryngol 2004; 113:43-45.
Shewan LG, Coats AJS, Henein M. Requirements for ethical publishing in biomedical journals. International Cardiovascular Forum Journal 2015;2:2. DOI 10.17987/icfj.v2il.4
Authors who publish with this journal agree to the following terms:
a. The authors will retain copyright under a Creative Commons Attribution License (CC-BY 4.0) that allows others to share the work with an acknowledgement of the work's authorship and initial publication in this journal.
b. Authors are able to enter into separate, additional contractual arrangements for the non-exclusive distribution of the journal's published version of the work (e.g., post it to an institutional repository or publish it in a book), with an acknowledgement of its initial publication in this journal.
c. Authors are permitted and encouraged to post their work online (e.g., in institutional repositories or on their website) prior to and during the submission process, as it can lead to productive exchanges, as well as earlier and greater citation of published work (See The Effect of Open Access).